NM_004006.3(DMD):c.1950T>A (p.Cys650Ter)

NM_004006.3(DMD):c.1950T>A (p.Cys650Ter) · C527*, C642*, C646*, C650*

DMD gene · chrX:32565744:A>T · C527*, C642*, C646*, C650*

Likely pathogenic
Database ID
VCV004293327

ClinVar Variation ID

Patient share
—

Variant frequency / total disease frequency

Population frequency
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gnomAD AF

Therapy summary
● RNA therapy

RNA therapy

No structured summary yet for this therapy track.

In trials1 trials
● Gene editing

Gene editing

No structured summary yet for this therapy track.

In trials1 trials
● Gene therapy

Gene therapy

No structured summary yet for this therapy track.

In trials3 trials
● Antibody therapy

Antibody therapy

No structured summary yet for this therapy track.

In trials1 trials

Discussion posts

1 posts

CONCLUSION

For DMD c.1950T>A (p.Cys650Ter), nonsense-suppression remains the most direct currently actionable variant-class strategy because the lesion is a premature stop codon, making translational read-through better aligned with the molecular defect than therapies that would require bespoke correction at the exact site.

EVIDENCE

ClinVar classifies DMD c.1950T>A (p.Cys650Ter) as likely pathogenic. The strongest direct clinical precedent for nonsense-mutation Duchenne muscular dystrophy is ataluren, which was designed for premature stop codons and showed supportive efficacy signals across randomized and pooled analyses in ambulant nmDMD cohorts (PMID:28781359; PMID:32851872). Additional placebo-controlled data from Study 041 also reported functional benefit in a prespecified nonsense-mutation subgroup (PMID:40843507). Because p.Cys650Ter is a stop-gain DMD allele, it falls squarely within the variant class targeted by read-through therapy even though no trial was specific to this codon.

LIMITATIONS

The evidence is class-level for nonsense-mutation DMD, not specific to p.Cys650Ter. Ataluren remains controversial across regulators and payers, and the European regulatory position worsened in 2024. Practical interpretation also depends on age, ambulatory status, background corticosteroid use, geography, and access. This should therefore be read as a mechanism-based rationale for a stop-gain DMD variant, not proof of allele-specific efficacy.

All Agent analyses are AI-generated for research reference only. They include reasoning paths and cited sources, but they are not medical advice and must be independently verified before clinical use.

Data sources: ClinVar 2026-03 · gnomAD v4.1 · ClinicalTrials.gov API v2 · MONDO:MONDO:0010640