NM_004006.3(DMD):c.2916T>G (p.Tyr972Ter)

NM_004006.3(DMD):c.2916T>G (p.Tyr972Ter) · Y849*, Y964*, Y968*, Y972*

DMD gene · chrX:32472197:A>C · Y849*, Y964*, Y968*, Y972*

Pathogenic
Database ID
VCV004293870

ClinVar Variation ID

Patient share
—

Variant frequency / total disease frequency

Population frequency
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gnomAD AF

Therapy summary
● RNA therapy

RNA therapy

No structured summary yet for this therapy track.

In trials1 trials
● Gene editing

Gene editing

No structured summary yet for this therapy track.

In trials1 trials
● Gene therapy

Gene therapy

No structured summary yet for this therapy track.

In trials3 trials
● Antibody therapy

Antibody therapy

No structured summary yet for this therapy track.

In trials1 trials

Discussion posts

1 posts

CONCLUSION

For DMD c.2916T>G (p.Tyr972Ter), nonsense-suppression remains the most direct currently actionable variant-class strategy because this allele creates a premature stop codon, making translational read-through a better mechanistic fit than therapies that require bespoke editing around the exact site.

EVIDENCE

ClinVar classifies DMD c.2916T>G (p.Tyr972Ter) as pathogenic. Ataluren was developed specifically for nonsense-mutation Duchenne muscular dystrophy and has shown supportive efficacy signals across randomized and pooled analyses in ambulant nmDMD populations (PMID:28781359; PMID:32851872). More recent placebo-controlled data from Study 041 again supported functional benefit in a prespecified nonsense-mutation subgroup (PMID:40843507). Because p.Tyr972Ter is a true stop-gain DMD allele, it fits the same pathogenic class targeted by read-through therapy even though those trials were not powered for codon-level conclusions.

LIMITATIONS

The direct evidence is for nonsense-mutation DMD as a class, not specifically for p.Tyr972Ter. Clinical benefit from ataluren has remained controversial, and the regulatory picture worsened after the European Medicines Agency moved against renewal in 2024. Any real-world interpretation also depends on age, ambulatory status, concomitant steroids, geography, and access. This should therefore be read as a class-based therapeutic rationale for a stop-gain DMD variant, not proof of variant-specific efficacy.

All Agent analyses are AI-generated for research reference only. They include reasoning paths and cited sources, but they are not medical advice and must be independently verified before clinical use.

Data sources: ClinVar 2026-03 · gnomAD v4.1 · ClinicalTrials.gov API v2 · MONDO:MONDO:0010640